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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Bile salt hydrolases
Dysferlin
Pharyngeal muscle
Sarcopenia
Agrégats de PABPN1
Annexin A2
Aggregate
Differentiation
Pax7
Human
Autoimmune diseases
RNA
Effector T cells
Muscle fibrosis
Actin
Atrophy
BINDING SPECIFICITY
Intercellular communication
Alphavirus
Myogenesis
Gene therapy
Muscular dystrophy
Antisens oligonucleotides
Dystrophie musculaire oculopharyngée
Geriatric assessment
Omics
Epigenetics
Thérapie génique
FSHD
Cross-bridge kinetics
DMD
Fibrosis
Mass spectrometry
Aav-U7
AUTOPHAGY
Adipose tissue
Neuromuscular disease
Myoblast
Satellite cell
Exon-skipping
Regenerative medicine
ALS
Autologous
Transcriptomics
Dystrophin
Anti-acetylcholine receptor antibodies
Cell therapy
Neuromuscular junction NMJ
Myositis
OPMD
DUX4
ARN
Xenograft
Arbovirus
Muscle strength
Functional genomics
Satellite cells
2-D PAGE
Accelerometry
AAV vectors
Lamins
APOPTOSIS
Myotube
DNA methylation
AAV
Alzheimer's disease
PABPN1 agregates
Amyotrophic Lateral Sclerosis
Muscle
Haploinsufficiency
Andermann syndrome
Dysferlinopathy
PABPN1
Oculopharyngeal muscular dystrophy
Duchenne muscular dystrophy
Triplet expansion disease
Myoblasts
MUTATIONS
Regeneration
Calcium
Akt
FAPs
Regulatory T cells
Metabolism
Anti-fibrotic pharmacotherapies
Antiserum
Gene replacement
AChR antibodies
Muscle dystrophy
Ageing
Aged
Myopathy
GENE
Muscle stem cells
Myopathies
Biomarker
Myosin
Skeletal muscle
Inflammation
Nuclear envelope